Does a Short QT Interval Presage a Short Life Span?

  • Antonis S Manolis Evagelismos General Hospital, Athens
  • Spyridon Koulouris Evagelismos Hospital, Athens, Greece
  • Kostas Kappos Evagelismos Hospital, Athens, Greece
Keywords: syncope, primary electrical disease, atrial fibrillation, sudden cardiac death, potassium channels, short QT syndrome

Abstract

A case of a 16-year old adolescent is presented who was referred for investigation of a syncopal episode. The ECG displayed a very short QT interval of 280 ms, compatible with the newly described short QT syndrome, which is genetic primary electrical disease of abnormal potassium currents responsible for the repolarization process of the cardiac muscle. The prognosis is similar to the other well known familial cardiac channelopathies, such as the long QT or the Brugada syndromes which are associated with a high risk of sudden cardiac death, requiring an implantable cardioverter defibrillator device for life-long protection.

Author Biography

Antonis S Manolis, Evagelismos General Hospital, Athens
Specialty: Cardiology
Published
2012-09-26
Section
Images in Medicine